FBPaseD article of interest

[tummyache]

Here is something recently published for those suspected of FPDaseD:

International practices in the dietary management of fructose 1-6 ...
ojrd.biomedcentral.com/articles/10.1186/s13023-018-0760-3
by A Pinto - ‎2018 - ‎Cited by 1 - ‎Related articles
Jan 25, 2018 - In fructose 1,6 bisphosphatase (FBPase) deficiency, management aims to ... the dietary prescriptions of 126 patients with FBPase deficiency.

[ukbill]

Useful info. 1g per Kg of uncooked Cornstarch to support blood sugar levels for 8 hours.. I was wondering how much was needed.
It also seems to describe the condition my daughter had as a baby.

[tummyache]

Sometimes, I use the corn starch drink in unsweetened rice milk to help with hypo. It's actually good for HFI, FBPaseD, and Glycogen Storage Disease (GSD - especially the types that involve the liver heavily) . All 3 are very closely related from the same carbohydrate pathway, although they come from different DNA gene anomalies. We all have similar symptoms -- especially the hypoglycemia.